Procedure Description:

Total Anomalous Pulmonary Venous Connection (TAPVC) Treatment

Depending on the particular issues with the blood vessel's anatomy, a different repair is suggested for TAPVR. The pulmonary veins that emerge from the lungs and the left atrium will usually be connected by the surgeon. Along with that, he or she will seal the blood vessel that it was previously emptying. An atria reconstruction may be necessary if the blood vessels are draining into the right atrium rather than the left. The left atrium will thereafter be the destination of the blood vessel drain. TAPVR causes the blood arteries in the lungs to return to the heart in an unusual way. To address this issue, open cardiac surgery known as TAPVR is performed.

Disease Description:

TAPVR, or total anomalous pulmonary venous return, is a congenital cardiac condition. Vein connections are altered in TAPVR. The right atrium, the top chamber of the right heart, is where blood circulates. Oxygen-poor blood mixes with oxygen-rich blood due to this alteration in blood flow. The blood that is sent to the body as a result lacks sufficient oxygen. The location of the vein connections determines the particular type of TAPVR. Congenital heart illness is not a family history for the majority of babies born with TAPVR.

Disease Sign and Symptoms:

A newborn with TAPVR may have trouble breathing. The low oxygen levels in the baby's skin might make it appear gray or blue. We refer to this as cyanosis. TAPVR signs may be observed by a medical professional shortly after delivery. However, some kids don't have symptoms right away.

Most often, severe congenital cardiac abnormalities are discovered within the first few months of life or shortly after birth.

Symptoms and indicators could consist of: pale gray or blue fingernails, lips, or tongue (cyanosis), Breathing quickly, swelling in the stomach, legs, or surrounding the eyes, breathing difficulties during feedings, which prevents healthy weight gain.

Disease Causes:

It could be useful to comprehend how the heart normally functions in order to comprehend the reasons of congenital cardiac abnormalities.

There are two chambers on the right and two on the left of the heart. The left and right sides of the heart are used for various activities in order to pump blood throughout the body.

The pulmonary (lung) arteries carry blood from the right side of the heart to the lungs. Blood absorbs oxygen in the lungs and then travels through the pulmonary veins back to the left side of the heart. The blood is subsequently pumped by the left side of the heart into the aorta, the body's main artery, and throughout the body.

Disease Diagnosis:

The pediatrician examines your child physically and uses a stethoscope to listen to their heart. There can be a whooshing noise, known as a cardiac murmur.

The test used to identify complete abnormal pulmonary venous return is an echocardiography. This test projects images of the beating heart onto sound waves. The size of the heart chambers, any holes in the heart, and the pulmonary veins can all be seen on an echocardiography. Additionally, it displays blood flow via the heart's valves.

If more information is required, other tests like an electrocardiogram, a chest X-ray, or a CT scan might be performed.

Disease Treatment:

Typically, TAPVR requires surgery while the child is still a baby. Whether or whether there is a blockage determines when to perform surgery. Surgeons attach the pulmonary veins to the left upper chamber of the heart in order to heal it. Moreover, they seal the opening between the upper chambers of the heart.

For the rest of their lives, a person with total anomalous pulmonary venous return needs to have frequent checks to rule out infection, obstructions, or cardiac rhythm issues. Care should be given by a physician with expertise in congenital cardiac disorders. An expert in this field is known as a congenital cardiologist.